DOI: 10.5176/2345-7201_1.1.04
Authors: Cristine Catindig-Santelices M.D., Michael Joseph T. Reyes M.D., Melgar Matulac, M.D. Maycibel Macadaeg-Capero M.D., Frederick P. Gloria M.D.,
Abstract:
We report a case of a 25 year-old male with a functionally univentricular heart. He underwent consult for clearance prior to employment and has been asymptomatic since childhood with good functional capacity, his 6 minute walk test was normal at 300 meters. Pertinent physical findings were a right ventricular heave, a grade 3/6 systolic murmur over the 2nd-3rd intercostal spaces left parasternal border, a continuous murmur over the interscapular area and cyanosis of the nailbeds. Laboratory exams showed mild erythrocytosis and hypoxemia. Transthoracic and transesophageal echocardiographic findings showed a large ventricular septal defect (apical intraventricular septum remnant), atrioventricular discordance, malposition of the great arteries and severe pulmonary stenosis. Major aorto-pulmonary collaterals were demonstrated on hemodynamics study. Patient is stable and living a normal life but advised to avoid moderate to heavy strenuous activities. He is on a regular follow – up at our out patient clinic and there are no planned immediate surgical interventions at present.
Keywords: Univentricular Heart; Large Ventricular Septal Defect; Pulmonic Stenosis; Malposition of the Great Arteries, Major Aorto Pulmonary Collaterals
Updating...